The article presents a clinical case of successful surgical treatment of primary chondrosarcoma of the right ilium affecting the acetabulum and hip joint with acetabulum endoprosthesis. Rehabilitation measures aimed at restoration of the affected limb function are also described. After these measures, the patient demonstrated excellent functional results (93.3 % per the Musculoskeletal Tumor Society Score). Recurrence-free period was 49 months. In modern orthopedic oncology, many techniques of organ-preserving surgical treatment in patients with tumors of the periacetabular area with subsequent reconstruction are used but they are technically complex and carry high risks of postoperative complications. In our opinion, only combination of surgical techniques with interdisciplinary approach during perioperative rehabilitation allows to achieve good and even excellent functional results which is confirmed by the presented clinical case.